AATD + AUGa | AATD-AUGb | AATD PFTnormc | non-AATD COPDd | Healthye | |
---|---|---|---|---|---|
FVC (liters) | 3.85 ± 0.42 | 2.88 ± 0.16c | 4.27 ± 0.64e | 2.80 ± 0.32c,e | 3.96 ± 0.57d |
FVC (% pred) | 88 ± 6c | 79 ± 5c | 109 ± 6e | 77 ± 8c,e | 95 ± 6d |
FEV1 (liters) | 1.23 ± 0.25c,e | 1.35 ± 0.22c,e | 3.22 ± 0.47e | 1.49 ± 0.11c,e | 3.07 ± 0.35d |
FEV1 (% pred) | 35 ± 5c,e | 47 ± 7c,e | 107 ± 4e | 54 ± 7c,e | 93 ± 4d |
FEV1/FVC | 31 ± 3c,d,e | 47 ± 7c,e | 76 ± 7c,e | 56 ± 4c,e | 79 ± 2d |
FEV1/FVC (% pred) | 40 ± 4c,d,e | 61 ± 10c,e | 97 ± 2e | 71 ± 6c,e | 99 ± 3d |
Bike (two-legs) exercise | |||||
Watts | 62 ± 6c,e | 46 ± 11c,e | 176 ± 47d,e | 70 ± 11c,e | 126 ± 17d |
VO2peak (L/min) | 1.02 ± 0.11c,e | 0.69 ± 0.13c,e | 2.07 ± 0.51d | 1.16 ± 0.12c,e | 1.71 ± 0.25d |
VO2peak (ml/kg/min) | 12.6 ± 0.5c | 9.5 ± 1.1c,e | 26.9 ± 5.6d,e | 14.9 ± 1.7c | 20.3 ± 3.3 |
Knee extensor (single-leg) exercise | |||||
Watts | 25 ± 3c | 21 ± 7c | 59 ± 23d,e | 21 ± 3c | 26 ± 1 |
Smoking history | |||||
Never | 17% | 0% | 25% | 0% | 0% |
Ex-smoker | 83% | 100% | 75% | 43% | 100% |
Current | 0% | 0% | 0% | 57% | 0% |