Table 2 Symptoms and signs based on the items of BVAS

BVAS (total score)

19.0 (12.0–21.0)

16.5 (14.3–20.3)

0.906

General score

2.00 (0.00–2.00)

2.00 (1.25–2.00)

1.00

 Myalgia

0

2 (33 %)

0.143

 Arthralgia/Arthritis

2 (22 %)

0

0.486

 Fever >38 °C

6 (67 %)

4 (67 %)

1.00

 Weight loss >2 kg

1 (11 %)

0

1.00

Cutaneous score

0.00 (0.00–0.00)

0.00 (0.00–1.50)

0.351

 Skin vasculitis

1 (11 %)

2 (33 %)

0.525

Mucous membranes/eyes score

0.00 (0.00–3.00)

0.00 (0.00–0.00)

0.261

 Significant proptosis

1 (11 %)

0

1.00

 Scleritis

2 (22 %)

1 (17 %)

1.00

 Conjunctivitis

4 (44 %)

0

0.103

ENT score

4.00 (2.00–6.00)

5.50 (1.25–6.00)

0.806

 Bloody nasal discharge

6 (67 %)

1 (17 %)

0.119

 Paranasal sinus involvement

4 (44 %)

4 (67 %)

0.608

 Conductive deafness

3 (33 %)

2 (33 %)

1.00

 Sensorineural hearing loss

3 (33 %)

2 (33 %)

1.00

 Purulent nasal discharge*

4 (44 %)

0

0.103

 Suddle nose*

1 (11 %)

0

1.00

 Nasal septum perforation*

1 (11 %)

0

1.00

 Exudative otitis media*

3 (33 %)

3 (50 %)

0.622

Chest score

3.00 (3.00–6.00)

4.50 (3.00–6.00)

0.740

 Wheeze

0

1 (17 %)

0.400

 Nodules or cavities

8 (89 %)

6 (100 %)

1.00

 Pleural effusion

0

2 (33 %)

0.143

 Infiltrate

4 (44 %)

1 (17 %)

0.580

 Alveolar haemorrhage

0

0

NA

 Respiratory failure

0

1 (17 %)

0.400

 Cough*

2 (22 %)

5 (83 %)

0.0410

 Dyspnea*

0

0

NA

Renal score

4.00 (0.00–12.0)

4.00 (1.00–10.0)

0.851

 Hypertension

3 (33 %)

3 (50 %)

0.622

 Proteinuria >1+

5 (56 %)

2 (33 %)

0.608

 Haematuria >10 rbc/hpf

4 (44 %)

2 (33 %)

1.00

 Cr 125–249 μmol/L

0

1 (17 %)

0.40

 Cr 250–499 μmol/L

2 (22 %)

0

0.486

 Cr >500 μmol/L

2 (22 %)

1 (17 %)

1.00

 Rise in Cr >30 % or Ccr fall >25 %

4 (44 %)

1 (17 %)

0.58

 Hemodialysis*

2 (22 %)

1 (17 %)

1.00

Nervous system score

0.00 (0.00–0.00)

0.00 (0.00–0.00)

0.842

 Headache

1 (11 %)

1 (17 %)

1.00

 Hypertrophic pachymeningitis*

1 (11 %)

0

1.00

 Retro-orbital mass*

2 (22 %)

0

0.486