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Table 1 Cases of culture confirmed B. pseudomallei infection in CF

From: An international, multicentre evaluation and description of Burkholderia pseudomallei infection in cystic fibrosis

Patient

Year isolated

Location of acquisition

Country of residence

Age

Gender

CFTR Mutation

FEV1%

BMI

Co-pathogens

ETOH >40 g daily

Diabetes

1 (O’Carroll, 2003) [12]

1987

Northern Australia

Australia

21

M

F508del/F508del

49

21

Pseud

No

No

2

Early 1990’s

Northern Australia

Australia

40

M

F508del/R117

44.5

23

Pseud

Yes

No

Mycobacterium intracellulare

3 (Schülin, 2001) [14]

1992

Likely Thailand

Germany

31

M

Unknown

Unknown

Unknown

Unknown

Unknown

Unknown

4 (Visca, 2001) [15]

1998

South-East Asia

Italy

25

F

Unknown

Unknown

Unknown

Pseud

Unknown

Unknown

BCp

5 (Dance, 1999) [11]

1998

Malaysia

England

20

M

Unknown

Unknown

Unknown

Unknown

Unknown

Unknown

6 (Holland, 2002) [16]

1999

Northern Australia

New Zealand

8.5

M

G551D/1717-16 > A

46

15

Pseud

No

No

Aspergillus fumigatus

7 (Holland, 2002) [16]

2000

Northern Australia

New Zealand

7

F

G551D/1717-16 > A

Unknown

19

Haemophilus influenzae

No

No

Staph A

8 (O’Carroll, 2003) [12]

2000

Northern Australia

Australia

21

M

F508del/F508del

35

22

Pseud

No

Yes

Staph A

BCp

9a (Holland, 2002) [16]

2000

Northern Australia

Australia

18

M

F508del/F508del

45

21

Pseud

Yes

No

Staph A

BGl

Mycobacterium intracellulare

Other

10 (O’Carroll, 2003) [12]

2001

Northern Australia

Australia

14

M

F508del/G542X

80

17

Pseud

No

No

Staph

11 (Holland, 2002) [16]

2001

Northern Australia

New Zealand

38

M

F508del/F508del

36

19

Pseud

No

IFG

Staph A

12 (O’Carroll, 2003) [12]

2001

Northern Australia

Australia

25

F

Unknown

80

20

Pseud

No

No

Staph A

BCp

13 (Asiah, 2006) [8]

2004

Malaysia

Malaysia

17

M

Unknown

Unknown

Unknown

Pseud

Unknown

Unknown

Staph A

14 (Barth, 2007) [9]

2005

Brazil

Brazil

17

F

Unknown

Unknown

Unknown

Pseud

Unknown

Unknown

Staph A

15

2005

Thailand

England

30

F

Unknown

56

21

Pseud

No

Yes

Staph A

Aspergillus fumigatus

16 (Corral, 2008) [10]

2006

British Virgin Islands

England

17

M

F508del/E60X

63

22

Pseud

Unknown

No

Staph A

Canada

17

2007

Northern Australia

Australia

38

M

F508del/F711 + 5G > A

29

19

Pseud

No

No

Staph A

Aspergillus terreus

18

2007

Thailand

New Zealand

10

F

F508del/17aa + IG74

107

16

Pseud

No

No

Staph A

Other

19

2008

Thailand

Australia

22

F

F508del/F508del

85

23

Pseud

Yes

Yes

20 (O’Sullivan, 2011) [13]

2009

Aruba

USA

7

F

F508del/F508del

88

13

None

No

No

21

2010

Vietnam/Cambodia

England

23

F

F508del/F508del

44

19

Pseud

No

No

Haemophilus influenzae

22 (Radhakrishna, 2014) [17]

2011

Thailand

Australia

25

M

Unknown

95

24

Pseud

Unknown

No

Aspergillus fumigatus

23

2012

Malaysia/Philippines

Malaysia

19

M

R553X/unknown

18

17

Pseud

No

No

24

2013

Thailand/Japan

England

30

M

F508del/E60X

67

23

Pseud

No

No

25

2015

Thailand

England

21

F

F508del/F508del

71

18

Pseud

No

No

Staph A

  1. Pseud Pseudomona aeruginosa, Staph A Staphylococcus aureus, BCp Burkholderia cepacia complex, BGl Burkholderia gladioli, IFG impaired fasting glucos
  2. a3 distinct B. pseudomallei infections were recorded in this patient over 8 years