Clinical characteristics | n = 12 |
 Male/female | 5/7 |
 Age at initial visit [years] | 62 (47–75) |
 Acute onset/chronic onset | 8/4 |
 Smoking status (current or former/never smoker) | 6/6 |
Serological findings (reference value) | n = 12 |
 CK [U/L] (62–287) | 140 (17–672) |
 LDH [U/L] (70–139) | 252 (212–337) |
 ESR [mm/h] (2–10) | 38 (17–116) |
 CRP [mg/dl] (0–0.1) | 0.63 (0.03–1.79) |
 KL-6 [U/ml] (0–500) | 991 (514–3208) |
 SP-D [ng/ml] (0–110) | 232.3 (56.1–723.1) |
 PaO2 [Torr] (74–108) | 71.5 (53.0–84.5) |
Pulmonary functions | n = 11 |
 FVC % predicted [%] | 71.5 (42.4–86.1) |
 DLCO % predicted [%] | 66.1 (56.0–112.2) |