From: Effect of pulmonary arteriovenous malformations on the mechanical properties of the lungs
AGE (years) | 44.4 ± 16.7 |
MALE SEX (%) | 60 (38.7%) |
MUTATION | |
ENG | 56 (36.1%) |
ACVRL1/ALK1 | 85 (54.8%) |
Smad 4 | 2 (1.3%) |
No mutation found | 12 (7.7%) |
PAVMs | |
None | 88 (56.8%) |
1-3 PAVMs | 45 (29.0%) |
≥ 4 PAVMs | 22 (14.2%) |
TLC (% predicted) | 99.3 ± 11.8 (n = 151) |
RV (% predicted) | 102.5 ± 26.0 (n = 151) |
VC (% predicted) | 102.1 ± 13.3 (n = 155) |
FEV1 (% predicted) | 101.6 ± 12.9 (n = 155) |
FEV1/VC (%) | 83.8 ± 11.8 (n = 155) |
FEF75 (% predicted) | 79.8 ± 29.5 (n = 154) |
A-a O2 gradient (mmHg) | 12.4 ± 10.9 (n = 151) |