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Table 1 Subject characteristics at baseline

From: Pulmonary exacerbations and clinical outcomes in a longitudinal cohort of infants and preschool children with cystic fibrosis

Demographics
Female: Male 13:17
Age at first visit in years, median (range) 1.5 (0.2, 4.9)
Genotype
 F508/F508 17 (57%)
 F508/Other 10 (33%)
High risk genotype, n = 29a 28 (96%)
Method of diagnosisb
 Diagnosed by newborn screen 25 (83%)
 Meconium ileus 5 (17%)
 Clinical diagnosis 2 (7%)
Oropharyngeal culture results
 Negative culture 16 (53%)
Staphylococcus aureus 11 (36%)
Pseudomonas aeruginosa 0 (0%)
Haemophilus influenzae 6 (20%)
Weight z-score, median (range), n = 29 −0.36 (−2.3, 0.91)
Pancreatic insufficient, n = 30 30 (100%)
  1. aIn one patient a second mutation has not been identified
  2. bThree patients were diagnosed by both meconium ileus and a positive newborn screen