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Table 1 Subject characteristics at baseline

From: Pulmonary exacerbations and clinical outcomes in a longitudinal cohort of infants and preschool children with cystic fibrosis

Demographics

Female: Male

13:17

Age at first visit in years, median (range)

1.5 (0.2, 4.9)

Genotype

 F508/F508

17 (57%)

 F508/Other

10 (33%)

High risk genotype, n = 29a

28 (96%)

Method of diagnosisb

 Diagnosed by newborn screen

25 (83%)

 Meconium ileus

5 (17%)

 Clinical diagnosis

2 (7%)

Oropharyngeal culture results

 Negative culture

16 (53%)

Staphylococcus aureus

11 (36%)

Pseudomonas aeruginosa

0 (0%)

Haemophilus influenzae

6 (20%)

Weight z-score, median (range), n = 29

−0.36 (−2.3, 0.91)

Pancreatic insufficient, n = 30

30 (100%)

  1. aIn one patient a second mutation has not been identified
  2. bThree patients were diagnosed by both meconium ileus and a positive newborn screen