Table 1 Patient baseline characteristics

N

16

Sex (male/female)

7/9

Age (years)

23 (22, 25)

BMI (kg m^− 2)

20 (18, 21)

Cystic fibrosis-related diabetes (N (%))

8 (50)

Pancreatic insufficiency (N (%))

13 (81)

Chronic Pseudomonas aeruginosa infection (N (%))

7 (44)

FEV₁ (% predicted)

52 (43, 72)

DLNO (% predicted)

59 (51, 73)

DLCO (% predicted)

82 (69, 86)

V’O_2peak (mL kg^− 1 min^− 1)

32.0 (30.3, 34.4)

Mechanical power (W kg^− 1)

2.9 (2.3, 3.1)

HR_peak (beats min^− 1)

167 (163, 179)

RER

1.20 (1.15, 1.26)