Determinants of prognosis | Score 0 | Score 1 | Score 2 |
---|---|---|---|
WHO functional class | I, II | III | IV |
6MWD | > 440 m | 165-440 m | < 165 m |
NT-proBNP | NT-proBNP < 300 ng/l | NT-proBNP 300–1400 ng/L | NT-proBNP > 1400 ng/L |
Echocardiography | RA area < 18 cm2 | RA area 18–26 cm2 | RA area > 26 cm2 |
Total score | 0–2 → Low-risk stratum → One-year survival rate 95–100% | ||
3–5 → Intermediate-risk stratum→One-year survival rate 90–95% | |||
6–8 → High-risk stratum→One-year survival rate < 90% |