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Table 1 The modified risk assessment score of PAH

From: A modified risk score in one-year survival rate assessment of group 1 pulmonary arterial hypertension

Determinants of prognosis

Score 0

Score 1

Score 2

WHO functional class

I, II

III

IV

6MWD

> 440 m

165-440 m

< 165 m

NT-proBNP

NT-proBNP < 300 ng/l

NT-proBNP 300–1400 ng/L

NT-proBNP > 1400 ng/L

Echocardiography

RA area < 18 cm2

RA area 18–26 cm2

RA area > 26 cm2

Total score

0–2 → Low-risk stratum → One-year survival rate 95–100%

3–5 → Intermediate-risk stratum→One-year survival rate 90–95%

6–8 → High-risk stratum→One-year survival rate < 90%

  1. PAH pulmonary arterial hypertension, WHO world health organization, 6MWD 6-min walking distance, BNP brain natriuretic peptide, RA right atrial