Table 1 Clinical features of cases that describe EGPA and GPA overlap syndrome

Henochowichz 1986 [24]

25 F

J, K, L (AH), N, Sk

no

P: yes, K/N: yes

N/A

Cs, CTX

Yousem 1989 [10]

71 F

E, L, N, S

yes

P: no, L: yes

N/A

Cs, AZA

Krupsky 1993 [16]

43 M

J, L, Ne, S, Sk

no

P: yes, L: yes

+cANCA

Cs, CTX

Potter 1999 [25]- Case 1

29 M

J, L (AH), N, S

no

P: yes, L: yes

+cANCA, +PR3, neg pANCA

Cs, MTX, TMP-SMX

Potter 1999 [25]- Case 2

39 F

J, L (AH), S

no

P: yes, L: yes

+cANCA, +PR3, neg pANCA

Cs, MTX, CTX, TMP-SMX

Lane 2002 [14]- Case 1

N/A

L, K

N/A

K: yes

+cANCA

N/A

Lane 2002 [14]- Case 2

N/A

L, K, N, S

N/A

K: yes

+cANCA, +PR3

N/A

Lane 2002 [14]- Case 3

N/A

L, K, N, S

N/A

P: yes, K: yes

+cANCA

N/A

Lane 2002 [14]- Case 4

N/A

L, K

N/A

P: yes, K: yes

+cANCA, +PR3

N/A

Lane 2002 [14]- Case 5

N/A

L, K

N/A

K: yes

+cANCA

N/A

Kamali 2003 [15]

21 F

J, K, L (AH), Sk

no

P: yes

+cANCA, +PR3

Cs, CTX, IVIG

Shoda 2005 [13]

25 F

E, J, L (AH), N, S, Sk

no

P: yes, L/N: yes

+cANCA, +PR3, neg pANCA

Cs, MTX, CTX

Uematsu 2014 [8]

78 F

L (AH), S, Sk

no

P: yes

+cANCA, +PR3, neg pANCA

Cs, CTX

Surendran 2017 [9]

45 F

E, J, L (AH), K, N, Ne

yes

P: no

+cANCA, +PR3

Cs, CTX

Our Patient 2017

50 F

L (AH), Ne, S

yes

P: yes, L: yes

neg

Cs, AZA, IL-5