Table 1 Baseline characteristics of both patients at time of diagnosis
Patient 1 | Patient 2 | |
|---|---|---|
Age (years) | 55 | 55 |
Genotype | F508del and R117H-7T | |
BMI (kg/m2) | 20 | 21.1 |
FEV1 (L) | 0.78 | 2.13 |
FEV1 (%pred.) | 27.3 | 74 |
FVC (L) | 1.90 | 2.99 |
FVC (%pred.) | 52.8 | 82 |
MMEF 75/25 (%pred.) | 9 | 44 |
Sweat chloride (mmol/L) | 52 | 44 |
Elastase (μg/g stool) | 448 | > 500 |