Table 1 Baseline characteristics of patients with idiopathic pulmonary fibrosis
Clinical characteristics | n = 303 |
|---|---|
Age, years | 67.2 ± 9.5 |
Male sex | 234 (77.2%) |
BMI, kg/m2, median (IQR) | 22.7 (20.1–24.9) |
Ever-smoker | 211 (69.6%) |
Smoking, pack-years, median (IQR) | 30.0 (20.0–42.0) |
Underlying disease | |
 Hypertension | 100 (33.0%) |
 Diabetes mellitus | 88 (29.0%) |
 Pulmonary tuberculosis | 43 (13.2%) |
 Emphysema | 39 (12.9%) |
 Ischemic heart disease | 29 (9.6%) |
 Congestive heart failure | 10 (3.3%) |
GAP score, median (IQR) | 3.0 (2.0–4.0) |
6MWD, m, median (IQR) | 400.0 (308.5–480.0) (N = 152) |
Pulmonary function at diagnosis | |
 FVC, %, median (IQR) | 74.0 (59.0–86.0) |
 FEV1, %, median (IQR) | 88.0 (71.0–100.0) |
 FEV1/FVC, %, median (IQR) | 83.0 (77.8–89.0) |
 DLCO, % | 69.0 (51.0–86.0) |
Echocardiography | |
 Ejection fraction %, median (IQR) | 66.0 (61.0–70.0) (N = 196) |
 Right ventricular pressure, mmHg, median (IQR) | 28.0 (28.0–47.0) (N = 163) |
Chest CT | |
 mPA diameter, mm, median (IQR) | 27.9 (26.1–30.5) |
 Ascending Ao diameter, mm, median (IQR) | 34.2 (31.6–36.7) |
 mPA/Ao ratio, median (IQR) | 0.83 (0.77–0.90) |