Fig. 4From: Clinical characteristics of patients with familial idiopathic pulmonary fibrosis (f-IPF)Pedigree chart three. Generations (I-VI) with 42 members, index patient IV: 6. Abbreviations: def. IPF = definitive idiopathic pulmonary fibrosis, Heart-Dis = heart disease; OP = operation; DPLD = diffuse parenchymal lung disease; CD = cause of death; Laryngeal Ca = laryngeal carcinoma; FD = initial diagnosis year / age at first diagnosis in years; rapidly prog. IPF = rapidly progressive idiopathic pulmonary fibrosis; resp. insuff. = respiratory insufficiencyBack to article page