Table 3 Recorded ILD diagnoses in completed data sets (n = 705) up to 1st August 2019
ILD classification | ILD diagnosis | Total number of patients to 1st August 19 |
|---|---|---|
Idiopathic Interstitial | Idiopathic Pulmonary Fibrosis (IPF) | 240 (34%) |
Pneumonias (IIP) | Non-specific interstitial pneumonia (iNSIP) | 29 (4.1%) |
Desquamative Interstitial Pneumonia (DIP) | 2 (0.3%) | |
Combined Pulmonary Fibrosis and Emphysema (CPFE) | 30 (4.3%) | |
Cryptogenic Organising Pneumonia (COP) | 14 (2%) | |
Lymphocytic Interstitial Pneumonia (LIP) | 2 (0.3%) | |
Respiratory Bronchiolitis Associated ILD (RB-ILD) | 9 (1.3%) | |
Acute interstitial pneumonia (AIP) | 1 (0.1%) | |
Unclassifiablea | 51 (7.2%) | |
ILD of known association | Connective Tissue Disease associated ILD (CTD-ILD) | 125 (17.7%) |
Drug induced ILD | 7 (1.0%) | |
Occupational exposures | 11 (1.6%) | |
Granulomatous ILD | Hypersensitivity Pneumonitis (HP) | 66 (9.4%) |
Sarcoidosis | 44 (6.2%) | |
Vasculitis associated ILD | 12 (1.7%) | |
Miscellaneous ILD | Lymphangioleiomyomatosis (LAM) | 2 (0.3%) |
Langerhan’s cell histiocytosis (LCH) | 1 (0.1%) | |
Other | Early ILD – Interstitial Lung Abnormality | 5 (0.7%) |
Interstitial Pneumonia with Autoimmune features (IPAF) | 3 (0.4%) | |
Pulmonary Alveolar Proteinosis | 1 (0.1%) | |
Not ILDb | 18 (2.6%) | |
Not specified | 32 (4.8%) |