Fig. 2
Change over 24 months of follow-up in: a) FVC % of predicted; b) TLCO % of predicted; c) 6MWT distance. Change from baseline was calculated as a follow-up time point value minus the baseline value, therefore negative value indicates a decrease from baseline. Data are presented as median (IQR) values. Abbreviations: FVC – forced vital capacity, TLCO – transfer factor of the lung for carbon monoxide, 6MWT – six-minute walk test