Patient-year | Events | MR | 95 CI | |
---|---|---|---|---|
All cause mortality | 249 | 16 | 64.3 | 39.4–104.9 |
Sex | ||||
Women | 189 | 10 | 52.8 | 28.4–98.2 |
Men | 60 | 6 | 100.7 | 45.2–224.2 |
Age at diagnosis, years: | ||||
< =60 | 27.4 | 0 | – | – |
61–74 | 120 | 5 | 41.6 | 17.3–100 |
> =75 | 101 | 11 | 108.6 | 60.1–195.6 |
Center | ||||
FJD | 94 | 7 | 74.5 | 35.5–156.4 |
HCSC | 155 | 9 | 58.1 | 30.2–11.6 |
Positive rheumatoid factor | ||||
No | 22 | 0 | – | – |
Yes | 227 | 16 | 67.0 | 40.4–11.2 |
Smokers | ||||
Never | 115 | 7 | 61.0 | 29.1–128.0 |
Active and formers | 126 | 9 | 71.3 | 37–137 |
Missing data | 8 | 0 | – | – |
PTF parameters: | ||||
DLCO%: | ||||
< 60 | 91.5 | 10 | 109.3 | 58.5–2.3.2 |
> 60 | 154.5 | 6 | 38.8 | 17.4–86.4 |
Missing data | 3 | 0 | – | – |
Radiographic ILD pattern | ||||
UIP | 131 | 13 | 98.6 | 57.3–169.9 |
NSIP | 83 | 3 | 36.4 | 11.7–112.8 |
Others | 35 | 0 | – | – |