Fig. 5From: Pulmonary fibrosis in dyskeratosis congenita: a case report with a PRISMA-compliant systematic reviewKaplan–Meier survival analysis of telomere maintenance gene mutations in DC-related PF patients. Patients with mutations in TINF2 gene or DKC1/NHP2 gene had significantly worse transplant-free survival than those with variants in TERC/TERT/RTEL1/PARN gene (TINF2 gene vs TERC/TERT/RTEL1/PARN gene p = 0.013; DKC1/NHP2 gene vs TERC/TERT/RTEL1/PARN gene p = 0.027); No survival difference between TINF2 gene and DKC1/NHP2 gene was found (p = 0.684)Back to article page