From: Pulmonary fibrosis in dyskeratosis congenita: a case report with a PRISMA-compliant systematic review
CT patterns
Histopathological patterns
UIP (n = 6)
Probable UIP (n = 1)
Not-UIP (n = 2)
Possible UIP (n = 1)
UIP (n = 3)
3
0
1
Compatible with NSIP (n = 2)
Inconsistent with UIP (n = 4)