COPD | OHS | NMD | Non-CF BC or TB | SCOLIOSIS | ALS | Other Diagnoses | ||
---|---|---|---|---|---|---|---|---|
n | 388 | 264 | 180 | 92 | 65 | 58 | 58 | |
AGE (years) | mean (SD) | 65.6 (10) | 56.8 (14.4) | 31.5 (15.1) | 52.4 (19.1) | 53.3 (19) | 55.5 (12.1) | 53.7 (20.5) |
FEMALE | n (%) | 195 (50.3) | 157 (59.5) | 73 (40.6) | 56 (60.9) | 40 (61.5) | 19 (32.8) | 32(55.2) |
BMI | mean (SD) | 33.9 (10.1) | 47.3 (9.6) | 22.5 (6.8) | 30.3 (8.8) | 27.1 (8.4) | 23 (4.4) | 29.6(7.9) |
Patients progression | ||||||||
ACTIVE | n (%) | 203 (52.3) | 196 (74.2) | 136 (75.6) | 43 (46.7) | 49 (75.4) | 22 (37.9) | 26 (44.8) |
DEAD | 144 (37.1) | 39 (14.8) | 37 (20.6) | 38 (41.3) | 13 (20) | 31 (53.5) | 27 (46.6) | |
DISCHARGED | 41 (10.6) | 29 (11) | 7 (3.9) | 11 (12) | 3 (4.6) | 5 (8.6) | 5 (8.6) | |
Lung function | ||||||||
FVC (%) | mean (SD) | 59.2 (19.4) | 69.1 (20.7) | 36.7 (25.2) | 49.7 (14.5) | 36.1 (15.0) | 45.5 (12.1) | 46.2 (19.6) |
FEV1 (%) | 37.2 (18.5) | 67.7 (21.3) | 38.2 (25.3) | 32.9 (12.4) | 34.0 (13.0) | 48.0 (14.3) | 37.5 (20.4) | |
FEV1/FVC (%) | 49,7 (16.3) | 79 (10.1) | 89.4 (13) | 55.2 (14.2) | 81.3(12.2) | 83 (10.3) | 67.1 (20.5) | |
Arterial blood gas | ||||||||
paO2 (mmHg) | mean (SD) | 59.9 (14.1) | 64 (15) | 78.1 (21.2) | 61 (14.4) | 66.3 (17.7) | 80.2 (17.8) | 73.7 (25.8) |
paCO2 (mmHg) | 61 (10) | 59.2 (10.9) | 53.9 (14.6) | 61.5 (10.4) | 61.9 (12.8) | 53.5 (16.7) | 57.1 (11.4) | |
HCO3− (mmol/L) | 32.7 (5.6) | 31.6 (6.5) | 29.2 (6.2) | 33.5 (5) | 34.1 (9.9) | 28.5 (4.8) | 32.9 (4.3) | |
Type of ventilation | ||||||||
NIV | n (%) | 388 (100) | 264 (100) | 142 (78.9) | 92 (100) | 64 (98.5) | 41 (70.7) | 55 (94.8) |
TIV | 0 | 0 | 38 (21.1) | 0 | 1 (1.54) | 17(29.3) | 3 (5.17) | |
Time in HMV (months) | mean (SD) | 32 (29.7) | 42.3 (32.4) | 32.5 (26.4) | 34.7 (30.9) | 46.1(33.3) | 14.8 (10.4) | 22.9 (22) |
Compliance (h/day) | ||||||||
0–8 | (%) | 70.8 | 85.5 | 44.6 | 61 | 73.3 | 18.42 | 67.9 |
> 8 hasta 16 | 27.9 | 14.5 | 38.8 | 39 | 24.4 | 36.84 | 25 | |
> 16 | 1.3 | 0 | 16.5 | 0 | 2.2 | 44.74 | 7.14 | |
Ventilator settings | ||||||||
IPAP | mean (SD) | 16.6 (3.3) | 17.7 (3) | 16.5 (4.7) | 17.2 (3.6) | 15.1 (3.3) | 15.5 (4.2) | 17.1 (3.9) |
EPAP | 7.5 (1.3) | 7.9 (1.4) | 6.5 (1.3) | 7.6 (1.4) | 6.6(1,4) | 6.6 (1.3) | 7.4 (1.3) | |
Backup frequency rate | 15.5 (2.5) | 15.2 (2.1) | 15 (3.1) | 14.7 (2.3) | 15.3(2.5) | 16.4 (3.9) | 15.4 (2.9) |