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Table 4 Reported relative types in familial ILD

From: Clustering of lung diseases in the family of interstitial lung disease patients

 

All

Sarc

HP

IPF

uPF

non-IPF IIP

aidILD

oILD

Any ILD, n (%)

174

103

10

26

20

1

7

7

1st degree relative

125 (72)

64 (62)

9 (90)

23 (88)

17 (85)

1 (100)

6 (86)

5 (71)

Other relative

70 (40)

52 (50)

2 (20)

7 (27)

6 (30)

0

1 (14)

2 (29)

Only other relative

49 (28)

39 (38)

1 (10)

3 (12)

3 (15)

0

1 (14)

2 (29)

Sarcoidosis

109

90

4

3

5

0

3

4

1st degree relative

70 (64)

54 (60)

3 (75)

3 (100)

5 (100)

0

3 (100)

2 (50)

Other relative

49 (45)

46 (51)

1 (25)

0

0

0

0

2 (50)

Only other relative

39 (36)

36 (40)

1 (25)

0

0

0

0

2 (50)

Pulmonary fibrosis

54

7

5

22

15

0

4

1

1st degree relative

45 (83)

5 (71)

5 (100)

19 (86)

12 (80)

0

3 (75)

1 (100)

Other relative

15 (28)

2 (29)

1 (20)

7 (32)

4 (27)

0

1 (25)

0

Only other relative

9 (17)

2 (29)

0

3 (14)

3 (20)

0

1 (25)

0

Remaining ILD

20

11

1

2

3

1

0

2

1st degree

14 (70)

7 (64)

1 (100)

2 (100)

1 (33)

1 (100)

0

2 (100)

Other relative

7 (35)

5 (45)

0

0

2 (67)

0

0

0

Only other relative

6 (30)

4 (36)

0

0

2 (67)

0

0

0

  1. HP = hypersensitivity pneumonitis; IPF = idiopathic pulmonary fibrosis; uPF = unclassifiable pulmonary fibrosis; non-IPF IIP = idiopathic interstitial pneumonia other than IPF; aidILD = autoimmune ILD; oILD = other ILD. Familial disease is an ILD patient reporting one or more relatives with an ILD