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Table 4 Reported relative types in familial ILD

From: Clustering of lung diseases in the family of interstitial lung disease patients

  All Sarc HP IPF uPF non-IPF IIP aidILD oILD
Any ILD, n (%) 174 103 10 26 20 1 7 7
1st degree relative 125 (72) 64 (62) 9 (90) 23 (88) 17 (85) 1 (100) 6 (86) 5 (71)
Other relative 70 (40) 52 (50) 2 (20) 7 (27) 6 (30) 0 1 (14) 2 (29)
Only other relative 49 (28) 39 (38) 1 (10) 3 (12) 3 (15) 0 1 (14) 2 (29)
Sarcoidosis 109 90 4 3 5 0 3 4
1st degree relative 70 (64) 54 (60) 3 (75) 3 (100) 5 (100) 0 3 (100) 2 (50)
Other relative 49 (45) 46 (51) 1 (25) 0 0 0 0 2 (50)
Only other relative 39 (36) 36 (40) 1 (25) 0 0 0 0 2 (50)
Pulmonary fibrosis 54 7 5 22 15 0 4 1
1st degree relative 45 (83) 5 (71) 5 (100) 19 (86) 12 (80) 0 3 (75) 1 (100)
Other relative 15 (28) 2 (29) 1 (20) 7 (32) 4 (27) 0 1 (25) 0
Only other relative 9 (17) 2 (29) 0 3 (14) 3 (20) 0 1 (25) 0
Remaining ILD 20 11 1 2 3 1 0 2
1st degree 14 (70) 7 (64) 1 (100) 2 (100) 1 (33) 1 (100) 0 2 (100)
Other relative 7 (35) 5 (45) 0 0 2 (67) 0 0 0
Only other relative 6 (30) 4 (36) 0 0 2 (67) 0 0 0
  1. HP = hypersensitivity pneumonitis; IPF = idiopathic pulmonary fibrosis; uPF = unclassifiable pulmonary fibrosis; non-IPF IIP = idiopathic interstitial pneumonia other than IPF; aidILD = autoimmune ILD; oILD = other ILD. Familial disease is an ILD patient reporting one or more relatives with an ILD