Progression of pulmonary cysts in Birt-Hogg-Dubé syndrome: longitudinal thoracic computed tomography study with quantitative assessment

Table 1 Baseline characteristics of the study population

Characteristics		Value
Age (years)		54.2 ± 11.7
Sex	Male	41.9 (18)
Sex	Female	59.1 (25)
Smoking history (pack years)		6.6 ± 10.2
Pneumothorax history		51.2(22)
Pneumothorax number	0	48.8 (21)
	1	23.3 (10)
	2	11.6 (5)
	3	7.0 (3)
	4	7.0 (3)
	5	2.3 (1)
Family history of pneumothorax		27.9 (12)
Initial PFT	FEV1%pred	84.0 ± 13.3
	FEV1/FVC (%)	78.6 ± 7.5
	VC %pred	95.2 ± 14.9
	RV/TLC (%)	30.1 ± 6.4
	DLCO %pred	80.7 ± 11.6
	DLCO/VA (%)	93.2 ± 14.2

The mean ± standard deviation was used for continuous data, and the percentage and frequency were indicated for categorical data
PFT pulmonary function test, FEV1 forced expiratory volume in one second, FVC forced vital capacity, VC vital capacity, RV residual volume, TLC total lung capacity, DLco carbon monoxide transfer factor, DLco/VA carbon monoxide transfer coefficient, %pred percentage of predicted value capacity

ISSN: 1471-2466