Figure 4From: Idiopathic pleuroparenchymal fibroelastosis: consideration of a clinicopathological entity in a series of Japanese patients Clinical Course of the cases. Case 1 radiologically deteriorated a year after diagnosis (a, b). Other cases present similar behavior. (c) Decrease in FVC was confirmed in all cases during the follow up. The median follow up was 12.1 (range 4.37-22.2) months.Back to article page