Control | CFIP | UCTD-ILD | CTD-ILD | p-value | |
---|---|---|---|---|---|
Subjects, n | 26 | 19 | 16 | 33 | |
Age, years | 64 (59–81) | 67 (54–80) | 70 (53–79) | 63 (39–83) | 0.0265 |
Females, n (%) | 16 (61) | 3 (15) | 8 (50) | 22 (66) | 0.0032 |
Smoking status | |||||
Former smoker, n (%) | 7 (26) | 12 (63) | 8 (50) | 11 (33) | 0.0617 |
Current smoker, n (%) | 1 (3) | 2 (10) | 1 (6) | 0 (0) | 0.3250 |
Pack-years | 0 (0–40) | 30 (0–150) | 5 (0–70) | 0 (0–100) | 0.0035 |
Pa, O2 mmHg | 83.6 (62.4–111.7) | 72.5 (58.8–86.6) | 79.2 (42.3–105.2) | 0.1413 | |
KL-6, U · mL−1 | 261 (140–491) | 1581 (304–8298) | 1045 (363–4560) | 1117 (289–3943) | <0.0001 |
SP-D, ng · mL−1 | 32.3 (8.6–126.0) | 292.5 (32.3–1070) | 206.0 (88.6–405) | 175.0 (31.2–994.0) | <0.0001 |
BAFF, ng · mL−1 | 0.6 (0.5–0.9) | 1.0 (0.3–1.9) | 1.8 (1.0–2.3) | 2.0 (0.6–16.7) | <0.0001 |
VC, L | 1.9 (0.9–3.1) | 2.1 (0.9–3.1) | 2.0 (1.0–3.5) | 0.9213 | |
VC, % pred | 59.8 (35.4–128.2) | 69.2 (37.9–97.4) | 65.4 (41.3–104.1) | 0.3390 | |
DL,CO, mL · min−1 · mmHg−1 | 9.3 (3.4–15.4) | 8.9 (4.5–16.9) | 10.8 (4.6–16.9) | 0.6097 | |
DL,CO, %pred | 63.2 (43.5–125.4) | 60.4 (26.9–74.4) | 64.7 (29.0–109.4) | 0.2751 |