All Respondentsa N = 114 | Adult Programs N = 57 | Affiliate Programs N = 12 | Pediatric Programs N = 43 | |
---|---|---|---|---|
n (%) | n (%) | n (%) | n (%) | |
FEV1 < 30% predicted | 107 (94%) | 53 (93%) | 12 (100%) | 40 (93%) |
NPPV for hypercapnia | 96 (84%) | 51 (90%) | 11 (92%) | 33 (77%) |
Rapid decline in FEV1 | 90 (79%) | 40 (70%) | 10 (83%) | 38 (88%) |
Hemoptysis not controlled by embolization | 75 (66%) | 35 (61%) | 9 (75%) | 29 (67%) |
Supplemental oxygen | 64 (56%) | 29 (51%) | 9 (75%) | 26 (61%) |
Pulmonary hypertension | 62 (54%) | 34 (60%) | 9 (75%) | 19 (44%) |
Increasing frequency pulmonary exacerbations | 57 (50%) | 25 (44%) | 7 (58%) | 24 (56%) |
Refractory/recurrent pneumothorax | 53 (47%) | 26 (46%) | 9 (75%) | 18 (42%) |
Pulmonary exacerbation with ICU admission | 38 (33%) | 16 (28%) | 4 (33%) | 18 (42%) |
Skipped questionb | 2 (2%) | 1 (2%) | 0 | 1 (2%) |