Variable | Total population (n = 145) |
---|---|
Age | 51.9 ± 16.1 |
Sex, n (%) | |
Male | 34 (23.4) |
Female | 111 (76.6) |
IPAH, n (%) | 53 (36.6) |
HPAH, n (%) | 9 (6.2) |
Other comorbid conditions, n (%) | |
Systemic sclerosis | 26 (17.9) |
Mixed connective tissue disease | 9 (6.2) |
Systemic lupus erythematosus | 8 (5.5) |
Rheumatoid arthritis | 6 (4.1) |
Dermatomyositis | 1 (0.7) |
Human immunodeficiency infection | 1 (0.7) |
Portal hypertension | 11 (7.6) |
Atrial septal defect | 14 (9.7) |
Ventricular septal defect | 3 (2.1) |
Partial anomalous pulmonary venous return | 4 (2.8) |
WHO functional class, n (%) | |
Class I | 6 (4.1) |
Class II | 53 (36.6) |
Class III | 69 (47.6) |
Class IV | 17 (11.7) |
Right heart catheterization results | |
Mean PAP, mmHg | 41.4 ± 13.4 |
Mean PAWP, mmHg | 8.4 ± 3.7 |
PVR, Wood unit | 7.9 ± 5.5 |
CI, L/min/m2 | 3.2 ± 1.3 |