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Table 1 Clinical characteristics and laboratory data

From: Idiopathic pleuroparenchymal fibroelastosis: consideration of a clinicopathological entity in a series of Japanese patients

 

Case.1

Case.2

Case.3

Case.4

Case.5

Age (yr)/sex

70, male

74, female

67, male

67, male

72, male

Smoking status

Ex-smoker

Never-smoker

Never-smoker

Never-smoker

Never-smoker

BMI

18.7

17.5

15.9

17.9

17.0

Symptom

Dyspnea

Dyspnea

Cough

Dyspnea

Dyspnea

Crackles

+

-

-

-

+

BAL lym (%)

8.6

0

16

1

ND

 neu (%)

0.6

0

1.0

8

ND

  eos (%)

0

1

0

3

ND

KL-6 (U/ml)

410

604

437

1000

469

SP-D (ng/ml)

204

131

129

437

133

RF (U/ml)

54

-

4

1

16

ANA

-

×40

×40

-

-

PaO2 (Torr)

82

94.4

95.8

83.0

82.0

Prognosis

Survive 12 months

Survive 6 months

Survive 44 months

Survive 10 months

Survive 16 months

  1. Abbreviations: BMI, body mass index, BAL, broncho-alveolar lavage, KL-6, Sialylated carbohydrate antigen KL-6, Sp-D, Surfactant Protein D, RF , rheumatoid factor, ANA, antinuclear antibody.