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Table 2 Proportion of PAH subtypes at time of diagnosis

From: Epidemiology and long-term survival of pulmonary arterial hypertension in the Czech Republic: a retrospective analysis of a nationwide registry

PAH subtype All cases n = 191 Prevalent cases n = 100 Incident cases n = 91 p*
Idiopathic, n (%) 116 (60.7) 67 (67.0) 49 (53.8) 0.177
Heritable, n (%) 7 (3.7) 3 (3.0) 4 (4.4)
APAH-CHD, n (%) 39 (20.4) 16 (16.0) 23 (25.3)
APAH-CTD, n (%) 21 (11.0) 12 (12.0) 9 (9.9)
Other, n (%) 8 (4.2) 2 (2.0) 6 (6.6)
  1. APAH-CHD, pulmonary arterial hypertension associated with congenital heart disease; APAH-CTD, pulmonary arterial hypertension associated with connective tissue disease.
  2. Other PAH etiologies included: portal hypertension and PAH associated with hemolytic anemia.
  3. *Difference between prevalent and incident cases maximal likelihood chi-square test.