PAH subtype | All cases n = 191 | Prevalent cases n = 100 | Incident cases n = 91 | p*
|
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Idiopathic, n (%) | 116 (60.7) | 67 (67.0) | 49 (53.8) | 0.177 |
Heritable, n (%) | 7 (3.7) | 3 (3.0) | 4 (4.4) |
APAH-CHD, n (%) | 39 (20.4) | 16 (16.0) | 23 (25.3) |
APAH-CTD, n (%) | 21 (11.0) | 12 (12.0) | 9 (9.9) |
Other†, n (%) | 8 (4.2) | 2 (2.0) | 6 (6.6) |
- APAH-CHD, pulmonary arterial hypertension associated with congenital heart disease; APAH-CTD, pulmonary arterial hypertension associated with connective tissue disease.
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†Other PAH etiologies included: portal hypertension and PAH associated with hemolytic anemia.
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*Difference between prevalent and incident cases maximal likelihood chi-square test.