Epidemiology and long-term survival of pulmonary arterial hypertension in the Czech Republic: a retrospective analysis of a nationwide registry

Table 2 Proportion of PAH subtypes at time of diagnosis

PAH subtype	All cases n = 191	Prevalent cases n = 100	Incident cases n = 91	p^*
Idiopathic, n (%)	116 (60.7)	67 (67.0)	49 (53.8)	0.177
Heritable, n (%)	7 (3.7)	3 (3.0)	4 (4.4)
APAH-CHD, n (%)	39 (20.4)	16 (16.0)	23 (25.3)
APAH-CTD, n (%)	21 (11.0)	12 (12.0)	9 (9.9)
Other^†, n (%)	8 (4.2)	2 (2.0)	6 (6.6)

APAH-CHD, pulmonary arterial hypertension associated with congenital heart disease; APAH-CTD, pulmonary arterial hypertension associated with connective tissue disease.
^†Other PAH etiologies included: portal hypertension and PAH associated with hemolytic anemia.
^*Difference between prevalent and incident cases maximal likelihood chi-square test.

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