| Â | Initial investigation | After 2-year follow-up |
|---|
FVC | 4.58Â l (85%) | 4.82Â l (81%) |
FEV1 | 4.48Â l/min (101%) | 4.45Â l/min (93%) |
MEF50 | 7.32Â l/min (140%) | 7.17Â l/min (121%) |
TLC | 6.14Â l (92%) | 6.09Â l (78%) |
DLCO | 87% | 81% |
- Legend: The first examination was performed two weeks after disease manifestation, there were more than 10 tests performed in the follow-up, all showing similar values. The numbers are related to normal values (parenthesis); the reference cohort has changed during the follow-up (< 18 and > 18 years of age). The shape of expiratory/inspiratory flow curve suggested intermittently mild periphery obstruction. Abbreviations:FVC Forced vital capacity, FEV1 Forced expiratory volume in 1 second, MEF Maximal mid-expiratory flow, TLC Total lung capacity, DLCO Diffusing lung capacity.
