Table 1 Baseline characteristics of participants

Age of child (years)

n = 100

Median (range)

10.1 (0.2-18.6)

Gender

n = 100

% male

44

Ethnicity

n = 100

% Caucasian

100

FEV ₁ % predicted (in children over 6 years)

n = 71

FEV₁ ≥ 70% (mild disease)

57 (80.3%)

FEV₁ 40-69% (moderate disease)

11 (15.5%)

FEV₁ ≤ 39% (severe disease)

3 (4.2%)

Mean FEV₁% predicted (±95% C.I.)

84% (±4.54)

BMI percentile (children <18 years)

n = 98

<15^th percentile

10 (10.2%)

≥15^th percentile

88 (89.8%)

BMI (≥18 years)

n = 2

≥18.5 ≤ 25

2 (100%)

Swachman-Kulczycki radiological score/25

Median (IQR)

22 (20-23)

Colonisation status

n = 100

B.cepacia

5 (5% chronic)

Methicillin-resistant Staphylococcus aureus (MRSA)

7 (7% chronic)

P.aeruginosa ^†

3 (3% intermittent)

12 (12% chronic)

Days in hospital over the previous year

n = 100

Median (IQR)

0 (0-1.75)

Number of medications currently prescribed

n = 100

Median (IQR)

6 (4-8)

Enzyme supplement prescribed [n = %]

81 (81%)

Vitamins prescribed [n = %]

98 (98%)

Chest physiotherapy prescribed [n = %]

99 (99%)

Other medical diagnosis

No

84 (84%)

Yes

16 (16%)