Novel homozygous BMP9 nonsense mutation causes pulmonary arterial hypertension: a case report

BMC Pulmonary Medicine

Table 1 Cardiac catheterization data

Using the above values including an assumed VO2 of 155 ml/min/m2 and Hgb 11.4 g/dL, calculations were the following: Qp = 5.2 L/min/m2, Qs = 5.2 L/min/m2; Qp:Qs = 1:1, PVR 4.4 WU/m2. No significant changes noted in pressures while on O2, NO or during administration of isoproterenol
Abbreviations: RPA right pulmonary artery, LFA left femoral artery, S/D/M systolic, diastolic, mean artery pressures, RA right atrium, RV right ventricle, RPCW right pulmonary capillary wedge, CO cardiac output, CI cardiac index, Qp pulmonary blood flow, Qs systemic blood flow, PVR pulmonary vascular resistance

ISSN: 1471-2466