Table 1 Demographic and clinical data of the study cohorts

82 (10.9%)

130 (17.4%)

36 (4.8%)

26 (3.5%)

23 (3.1%)

452 (60.3%)

26 (7–69)

25 (6–48)

15 (6–36)

15 (5–29)

20 (9–45)

14 (4–56)

CFTR Genotype

phe508del/phe508del

6.8%

10.3%

2.8%

2.9%

1.7%

30.8%

phe508del/other

3.8%

6%

1.6%

0.4%

1.1%

24.3%

other

0.5%

0.8%

0.27%

0.13%

0.27%

4%

unknown

0.13%

0.27%

0.13%

0%

0%

1.2%

21.2^a (13.1–34.9)

20 (9–30.2)

19 (14.3–26.8)

18.7 (14.3–26.1)

19 (12.3–25.7)

18.9 (10.4–33.7)