Fig. 1

Kaplan-Meier survival curves for tertiles of baseline values of forced vital capacity (FVC %pred.) (a), diffusing capacity of the lung for carbon monoxide (DLCO %pred.) (b), 6-min walking distance (6MWD) (c) and steps per day (d) are displayed on the left. Longitudinal changes (i.e. baseline and follow-up values of survivors) of FVC %pred. (e), DLCO %pred. (f), 6MWD (g) and steps per day (h) are displayed as bar-charts on the right. In Kaplan-Meier survival curves solid lines represent the lowest tertile, dashed lines the mid tertile and dotted lines the highest tertile of the baseline values of FVC %pred. (a), DLCO %pred.(b), 6MWD (c) and steps per day (d), respectively. Censored data of surviving patients are represented as vertical dashes. P-values are presented within the single graphs. Bar-charts represent baseline (dark grey, left) and follow-up (light grey, right) data of FVC %pred. (e), DLCO %pred. (f), 6MWD (g) and steps per day (h). Comparissons between baseline and follow-up were made with paired t-tests and p-values were <0.001, 0.024, 0.055 and <0.001, respectively