Table 1 Baseline Characteristics and Outcomes
Variable | IPF Cohort (n = 216) | IPAF-UIP Cohort (n = 77) | Combined UIP Cohort (n = 293)a |
|---|---|---|---|
Age, mean (±SD) | 69.3 (7.8) | 63.3 (9.9) | 67.7 (8.8) |
Male Gender, n (%) | 160 (74.1) | 41 (53.3) | 201 (68.6) |
Race, n (%) | |||
 White | 182 (84.3) | 59 (76.6) | 241 (82.3) |
 African American | 15 (6.9) | 9 (11.7) | 24 (8.2) |
 Hispanic | 10 (4.6) | 8 (10.4) | 18 (6.1) |
 Asian | 9 (4.2) | 1 (1.3) | 10 (3.4) |
Any auto-antibody (+) | 93 (43.1) | 74 (96.1) | 167 (57.0) |
ANA (+) b | 84 (38.9) | 64 (83.1) | 148 (50.5) |
HRCT, n (%) | |||
 UIP | 156 (72.2) | 41 (54) | 197 (67.5) |
 Possible UIP | 36 (16.7) | 14 (18.4) | 50 (17.1) |
 Inconsistent with UIP | 24 (11.1) | 21 (27.6) | 45 (15.4) |
UIP by SLB c, n (%) | 93 (97.9) | 55 (100) | 148 (98.7) |
FVC (% pred), mean (±SD) | 67.5 (17.4) | 63.5 (16.9) | 66.5 (17.4) |
DLCO (% pred), mean (±SD) | 51.1 (17.1) | 48.1 (16.8) | 50.3 (17.1) |
GAP Score, mean (±SD) | 4.1 (1.6) | 3.7 (1.6) | 4.0 (1.6) |
Outcomes | |||
 Death | 108 (50) | 35 (45.5) | 143 (48.8) |
 Transplant | 14 (6.5) | 14 (18.2) | 28 (9.6) |