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Table 1 Characteristics of patients with myositis-associated ILD

From: Elevated α-defensin levels in plasma and bronchoalveolar lavage fluid from patients with myositis-associated interstitial lung disease

Characteristic

N (%)

Gender (male/female)

15/41

Age (y)

60 (range, 50–66)

Clinical diagnosis

 Polymyositis

7 (13%)

 Dermatomyositis

28 (50%)

 Clinically amyopathic dermatomyositis

21 (38%)

Myositis-specific autoantibodies

 anti-ARS Ab

26 (46%)

 anti-Jo-1 Ab

11 (20%)

 anti-PL-7 Ab

6 (11%)

 anti-KS Ab

3 (5%)

 anti-PL-12 Ab

2 (4%)

 anti-EJ Ab

2 (4%)

 anti-OJ Ab

2 (4%)

 anti-MDA5 Ab

10 (18%)

 anti-Ku Ab

2 (4%)

 anti-TIF1 gamma Ab

2 (4%)

 Unknown

16 (29%)

Total

56