Table 5 Disease manifestation and outcome in different f-IPF generations
From: Clinical characteristics of patients with familial idiopathic pulmonary fibrosis (f-IPF)
| Â | Generations | p- value | ||
|---|---|---|---|---|
Grandparents | Parents | Youngest generation | 2./3.Gen. | |
Affected persons [n] | 3 | 25 | 49 | Â |
Age at first diagnosis [years] [mean value, ± SD] | 72 ± - | 66 ± 13 | 58 ± 11 | 0.013 |
Age at death (years) [mean value, ± SD] | 79 ± 6 | 71 ± 10 | 66 ± 9 | 0.131 |
Male [%] | 33 | 48 | 59 | 0.504 |