Table 2 Radiological Features of Patients with BMPR2 mutations or biallelic EIF2AK4 variants
BMPR2 (N = 38) n(%) | EIF2AK4 (N = 11) n(%) | p value | |
|---|---|---|---|
Centrilobular ground glass opacification | 13(34.2) | 10(90.9) | 0.001* |
Interlobular septal thickening | 11(28.9) | 9(81.8) | 0.002* |
Mediastinal lymphadenopathy | 4(10.5) | 5(45.5) | 0.008* |
Three signs | 3(7.9) | 4(36.4) | 0.017* |
Two signs | 8(21.1) | 5(45.5) | 0.11 |
One sign | 3(7.9) | 2(18.2) | 0.32 |
None | 24(63.2) | 0 | – |