Table 1 Demographic features of patients with WHO group 1 PH, WHO group 2 PH, and hyperdynamic PH
|  | WHO group 1 PH n = 138 | WHO group 2 PH n = 33 | Hyperdynamic PH n = 31 | p value |
|---|---|---|---|---|
Age, years | 36.6 ± 11.6 | 39.9 ± 12.7 | 36.6 ± 11.6 | 0.239 |
Female, No. (%) | 135 (97.8) | 32 (97) | 31 (100) | 0.198 |
BMI, kg/m2 | 21.3 ± 3.1 | 22.1 ± 5.1 | 22.6 ± 2.9 | 0.785 |
Disease duration since onset of CTD, weeks | 41.8 ± 60.6 | 23.1 ± 48.0 | 35.0 ± 49.4 | 0.039 |
Dyspnea on exertion, No. (%) | 116 (84.1) | 27 (81.8) | 22 (71.0) | 0.235 |
Interstitial lung disease, No. (%) | 24 (17.4) | 3 (9.1) | 9 (29.0) | 0.112 |
Hypertension, No. (%) | 14 (10.1) | 0 (0) | 4 (12.9) | 0.090 |
Diabetes, No. (%) | 3 (2.2) | 1 (3.0) | 1 (3.2) | 0.653 |
Hyperthyroid, No. (%) | 2 (1.4) | 1 (3.0) | 0 (0) | 0.683 |
Hypothyroid, No. (%) | 13 (9.4) | 1 (3.0) | 4 (12.9) | 0.333 |
Pregnancy, No. (%) | 0 (0) | 0 (0) | 0 (0) | 1.000 |
Anemia (HGB < 90 g/L), No. (%) | 2 (1.5) | 3 (9.1) | 1 (3.2) | 0.056 |
Diagnosis of CTD, No. (%) | ||||
 SSc | 16 (11.6) | 3 (9.1) | 7 (22.6) | 0.259 |
 Other CTDs | ||||
  SLE | 81 (58.7) | 15 (45.5) | 12 (38.7) |  |
  SS | 18 (13.0) | 10 (30.3) | 4 (12.9) |  |
  RA | 3 (2.2) | 1 (3.0) | 0 (0) |  |
  PM/DM | 0 (0) | 2 (6.1) | 1 (3.1) |  |
  MCTD | 7 (5.1) | 0 (0) | 4 (12.9) |  |
  UCTD | 8 (5.8) | 2 (6.1) | 3 (9.7) |  |
  AOSD | 5 (3.6) | 0 (0) | 0 (0) |  |