Table 1 Patient demographic and clinical characteristics, n = 70

Age, years

32.71 ± 11.65 (18–71)

Sex

41 (59) male

Genotype n, (%)

 F508del homozygous

28 (40)

 F508del heterozygous

31 (44)

 Other

11 (16)

BMI, kg/m²

20.32 ± 3.41 (15–33)

ppFEV₁

43.27 ± 19.93 (16–99)

Pancreatic insufficiency n, %

45 (64)

CF-related diabetes n, %

22 (31)

P. aeruginosa positive n, %

52 (74)

Hospital n, %

 Inpatient

67 (96)

 Outpatient

3 (4)

Reasons for medical treatment n, %

 PEX

33 (47)

 Starting CFTR-Modulator Therapy

14 (20)

 IVAT

8 (11)

 Others

16 (22)

Marital status n,%

 Single

36 (51)

 In partnership / married

34 (49)