| MPO-ANCA nephritis with UIP pattern (n = 31) | IPF (n = 32) |
---|---|---|
Number of deaths | 17 | 13 |
Cause of death | ||
 Respiratory-related death | 9 (53) | 12 (92) |
  Acute exacerbation | 2 | 5 |
  Chronic respiratory failure | 1 | 5 |
  Pneumonia | 1 | 0 |
  Pneumothorax | 1 | 2 |
  Alveolar hemorrhage | 4 | 0 |
 Non-respiratory-related death | 8 (47) | 1 (8) |
  Sepsis | 3 | 0 |
  Cardiovascular disease | 4 | 1 |
  Others | 1a | 0 |